苯丙酮尿症患儿血苯丙氨酸浓度宜维持在A、0.06~0.12mmol(1~2mg/dl)B、0.06~0.24mmol(1~4mg/dl)C、0.12~0.24mmol/L(2~4mg/dl)D、0.12~0.48mmol/L(2~8mg/dl)E、0.12~0.6mmol/L(2~10mg/dl)
苯丙酮尿症患儿血苯丙氨酸浓度宜维持在
A、0.06~0.12mmol(1~2mg/dl)
B、0.06~0.24mmol(1~4mg/dl)
C、0.12~0.24mmol/L(2~4mg/dl)
D、0.12~0.48mmol/L(2~8mg/dl)
E、0.12~0.6mmol/L(2~10mg/dl)
相关考题:
患儿,男,现4个月,新生儿期进行筛查时发现苯丙氨酸浓度为10mg/dl,诊断为苯丙酮尿症,该患儿血中苯丙氨酸浓度应当维持在A、4mg/dl以下B、2~10mg/dlC、10~15mg/dlD、10~30mg/dlE、25~30mg/dl
苯丙酮尿症患儿作饮食控制治疗时应注意下列哪几点( )。A.幼儿应以淀粉类、蔬菜、水果等低蛋白质食物为主B.苯丙氨酸按30~50mg/(kg·d)供给C.血苯丙氨酸浓度维持在0.12~0.6mmol/L(2~10m9/dl)为宜D。饮食控制至少持续至青春期以后E.以上都不是
苯丙酮尿症患儿血苯丙氨酸浓度宜维持在A、0.06~0.12mmol/L(1~2m/L)B、0.06~0.24mmol/L(1~4mg/L)C、0.12~0.24mmol/L(2~4mg/L)D、0.12~0.48mmol/L(2~8mg/L)E、0.12~0.6mmol/L(2~10mg/L)
苯丙酮尿症患儿血苯丙氨酸浓度宜维持在A.0.06~0.12mmol/L(1~2mg/L)B.0.06~0.24mmol/L(1~4mg/L)C.0.12~0.24mmol/L(2~4mg/L)D.0.12~0.48mmol/L(2~8mg/L)E.0.12~0.6mmol/L(2~10mg/L)
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A.染色体核型为:46,XX(XY)/47,+21B.染色体核型为:45,XO/46,xxC.血苯丙氨酸浓度>0.24mmol/L(4mg/dl)D.染色体核型为:48,XXXYE.血清铜蓝蛋白值:50mg/L先天睾丸发育不全综合征
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苯丙酮尿症患儿血苯丙氨酸浓度宜维持在A、0.12~0.48mmol(2~8mg/dl)B、0.12~0.6mmol(2~10mg/dl)C、0.06~0.12mmol(1~2mg/dl)D、0.06~0.02mmol(1~4mg/dl)E、0.12~0.24mmol(2~4mg/dl)
患儿,男,现4个月,新生儿期进行筛查时发现苯丙氨酸浓度为10mg/dl,诊断为苯丙酮尿症,该患儿血中苯丙氨酸浓度应当维持在A.4mg/dl以下B.4~10mg/dlC.10~15mg/dlD.10~30mg/dlE.25~30mg/dl
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苯丙酮尿症患儿治疗后血苯丙氨酸浓度应维持在()A、0.06~0.12mmol/L(1~2mg/dl)B、0.06~0.24mmol/L(1~4mg/dl)C、0.12~0.24mmol/L(2~4mg/dl)D、0.12~0.48mmol/L(2~8mg/dl)E、0.12~0.6mmol/L(2~10mg/dl)
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单选题苯丙酮尿症患儿血苯丙氨酸浓度宜维持在()A0.06~0.12mmol(1~2mg/dl)B0.06~0.24mmol(1~4mg/dl)C0.12~0.24mmol/L(2~4mg/dl)D0.12~0.48mmol/L(2~8mg/dl)E0.12~0.6mmol/L(2~10mg/dl)
单选题肝豆状核变性()A染色体核型为:46,XX(XY)/47,+21B染色体核型为:45,XO/46,xxC血苯丙氨酸浓度0.24mmol/L(4mg/dl)D染色体核型为:48,XXXYE血清铜蓝蛋白值:50mg/L
单选题21-三体综合征()A染色体核型为:46,XX(或XY)/47,+21B血苯丙氨酸浓度>0.24mmol/L(4mg/dl)C染色体核型为:45,XO/46,XXD染色体核型为:48,XXXYE血清铜蓝蛋白值:50mg/L
单选题患儿,男,现4个月,新生儿期进行筛查时发现苯丙氨酸浓度为10mg/dl,诊断为苯丙酮尿症,该患儿血中苯丙氨酸浓度应当维持在()A4mg/dl以下B4~10mg/dlC10~15mg/dlD10~30mg/dlE25~30mg/dl
单选题苯丙酮尿症患儿血苯丙氨酸浓度宜维持在()A0.06~0.12mmol(1~2mg/dl)B06~0.24mmol(1~4mg/dl)C0.12~0.24mmol/L(2~4mg/dl)D0.12~0.48mmol/L(2~8mg/dl)E0.12~0.6mmol/L(2~10mg/dl)
单选题苯丙酮尿症患儿治疗后血苯丙氨酸浓度应维持在()A0.06~0.12mmol/L(1~2mg/dl)B0.06~0.24mmol/L(1~4mg/dl)C0.12~0.24mmol/L(2~4mg/dl)D0.12~0.48mmol/L(2~8mg/dl)E0.12~0.6mmol/L(2~10mg/dl)
单选题苯丙酮尿症患儿血苯丙氨酸浓度宜维持在()A0.06~0.12mmol/L(1~2m/L)B0.06~0.24mmol/L(1~4mg/L)C0.12~0.24mmol/L(2~4mg/L)D0.12~0.48mmol/L(2~8mg/L)E0.12~0.6mmol/L(2~10mg/L)